
What else it's
called
According
to the
Mayo Clinic, IPF (Idiopathic Pulmonary Fibrosis) is:
An older term, now confused because of the inclusion of diseases other than UIP
and patients with fibrosis due to known causes in earlier literature.
Used prior to the
widespread use of HRCT, IPF referred either to a clinical only, or
clinicopathologic
syndrome of interstitial lung disease, with features suggesting pulmonary fibrosis of
unknown cause. In retrospect, this group included patients with NSIP, DIP, AIP, EG,
BOOP, and HSP, as well as some patients with resolving organizing DAD and even
stable post-inflammatory fibrosis. Some articles included patients with
connective-tissue disorders and others did not. The term IPF also includes the group
reported by Turner-Warwick as cryptogenic fibrosing alveolitis (CFA) in the UK,
which had a mean survival of 5 years, with 20% of patients doing well at 10 years,
and 20-25% of patients having a favorable response to corticosteroid therapy.
"IPF"
also includes the group of patients with OLB’s studied by Bjoraker et al, which
proved to have diseases other than UIP in 1/3 of cases. "IPF" also includes the 15%
of patients described by Winterbauer who have a disease which "does not progress
clinically".
Confused Yet??
IPF by Many Other Names
If it's not
IPF according to the above definitions
BUT it's called one of the terms below --
it is still pulmonary fibrosis
It is still not something you
want !
Chronic diffuse fibrosing
Cryptogenic Fibrosing Alveolitis (CFA)
Diffuse Alveolar Disease (DAD)
Diffuse infiltrative pulmonary disease (DIPD)
Fibrosing alveolitis
Hamman-Rich Syndrome
Honeycomb lung
Honey lung
Idiopathic fibrosing alveolitis
Idiopathic interstitial fibrosis of lung syndrome
Shrinking Lung
Stiff Lung
Usual Interstitial Pneumonia (UIP) |
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